Cutaneous PAN and Common Variable Immunodeficiency: what causes what?
نویسندگان
چکیده
Background Cutaneous polyarteritis nodosa (c-PAN) is a necrotizing vasculitis of small and medium-sized vessels limited to the skin, characterized by the presence of subcutaneous nodular, painful, non purpuric lesions with or without livedo reticularis occurring predominantly in the lower extremities, with no systemic involvement. The cause of c-PAN is unknown: infectious agents in childhood and immunodeficiency in adults have been associated with the disease.
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